Tufted angioma (Angioblastoma) of eyelid in adults-report of two cases
نویسندگان
چکیده
UNLABELLED Tufted angioma, first recognized in Japanese literature as "Angioblastoma of Nagakawa", is a rare benign vascular tumour with a variable clinical presentation. It commonly manifests as a macule, papule or nodule in infancy or childhood in the region of the upper trunk and neck. Here in we report two cases of this rare progressive angioma as lesions of the eyelid in adults. Tufted angioma has a classical "cannon ball" like appearance of vascular tufts on histopathology. Immunohistochemical staining with actin highlights the spindly stromal cells surrounding the capillaries. Complete physical examination and haematological work up is recommended in patients with tufted angioma to exclude rare association of port wine stain and Kasabach-Merritt syndrome with this rare entity. To the best of our knowledge, our cases illustrate the first case report of tufted angioma presenting as an eyelid lesion. VIRTUAL SLIDES The virtual slide(s) for this article can be found here: http://www.diagnosticpathology.diagnomx.eu/vs/1230909536950947.
منابع مشابه
Tufted Angioma: A Retrospective Analysis of 45 Cases
Tufted angioma (known in Japanese literature as angioblastoma of Nakagawa) is an uncommon vascular tumor. Although histologically benign, tufted angioma may be disfiguring because of the disease’s potential for infinite proliferation and a predilection for the head and neck. There is a lack of epidemiological reports on tufted angioma among Taiwanese and also a dearth of therapeutic guidelines....
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©2017 by Anais Brasileiros de Dermatologia Dear Editor, Tufted angioma is a rare vascular tumor, with slow angiomatous proliferation, usually located in the skin and subcutaneous tissue. Its clinical presentation is of a solitary angiomatous tumor, usually located on the neck, upper trunk and extremities. It is more frequent in children, with no sex or racial predilection. The term tufted angio...
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